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[Intensive care problems in congenital polycystic lung abnormality]
Insights
This study reports on a 6-month-old infant with congenital honeycomb lung and tension cysts, who experienced acute cardiorespiratory insufficiency. Surgical intervention and cyst excision led to normal development after five years.
Area of Science:
- Pediatric Pulmonology
- Thoracic Surgery
Background:
- Congenital honeycomb lung is a rare cystic lung malformation.
- Bilateral tension cysts can lead to acute cardiorespiratory compromise in infants.
Observation:
- A 6-month-old infant presented with acute cardiorespiratory insufficiency due to bilateral tension cysts secondary to congenital honeycomb lung.
- Initial management involved chest drainage to stabilize intrathoracic pressure.
Findings:
- Surgical resection of the right lower lobe and left upper lobe, along with excision of multiple cysts, was performed.
- Despite postoperative complications, the child achieved normal development at a 5-year follow-up.
Implications:
- Early surgical intervention is crucial for managing polycystic lung malformations.
- Aggressive surgical management can lead to favorable long-term outcomes in infants with severe cystic lung disease.
Abstract:
The development of bilateral tension cysts in a 6-month-old child suffering from inborn honeycomb lung resulted in acute cardiorespiratory insufficiency. First of all, we succeeded in controlling the recurrent rises in intrathoracic pressure by puncturing and chest draining performed by suction and by the Bülau method. The child thus became fit to be operated on. The right lower lobe, and, 7 days later, the left upper lobe, were resected and multiple single cysts excised from both residual lungs. The postoperative course of the disease was not free from complications, but five years of follow-up showed that the child's general development had become normal. Possibilities of treatment of pulmonary insufficiency, a typical symptom of polycystic lung malformation, are discussed, and the necessity for an early operation is emphasised.