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Acute macular infarctions in pediatric patients with hemoglobin SS disease
Patrick Sy Lee1, Cesar Alfaro1, Rao Me1
1Kresge Eye Institute/Department of Ophthalmology, Visual and Anatomical Sciences, Wayne State University School of Medicine, 4717 St. Antoine Street, Detroit, MI, 48201, USA.
Purpose:
To report two cases of symptomatic posterior pole arterial occlusions in patients with hemoglobin SS disease.
Observations:
Two teenage patients with hemoglobin SS disease presented with visual distortions, and on dilated fundus examination and testing, they were found to have arterial occlusions involving the posterior pole. The patients were evaluated for stroke with head imaging and received exchange transfusion by hematology.
Conclusions And Importance:
This case series reports the unusual findings of arterial occlusions in the posterior pole resulting in areas of retinal whitening and ischemia in patients with HbSS. While sickle cell retinopathy is typically considered a peripheral retinal disease, these findings underscore the importance of vigilance when examining patients with sickle cell disease.
