[Ventricular diverticulum in Cantrell´s pentalogy: rare but not isolated entities]

María Concepción Rocha-Arrieta1, Antonio Arias-Díaz2, Enrique Felipe Soto Zárate1

  • 1Universidad de Cartagena. Cartagena, Colombia. Universidad de Cartagena Universidad de Cartagena Cartagena Colombia.

Insights

Pentalogy of Cantrell, a rare condition, can coexist with congenital cardiac diverticulum. This case highlights successful surgical management of a left ventricular diverticulum in a child with Pentalogy of Cantrell.

Area of Science:

  • Pediatric Cardiology
  • Congenital Malformations
  • Surgical Management

Background:

  • Pentalogy of Cantrell is a rare congenital condition involving defects in the pericardium, heart, diaphragm, sternum, and abdominal wall.
  • Congenital cardiac diverticulum is an infrequent cardiac malformation that can be associated with Pentalogy of Cantrell.

Observation:

  • A case report of a child diagnosed with Pentalogy of Cantrell is presented.
  • During follow-up, the child was diagnosed with a left ventricular diverticulum.

Findings:

  • The left ventricular diverticulum associated with Pentalogy of Cantrell required surgical intervention.
  • The surgical management resulted in a favorable outcome for the patient.

Implications:

  • Timely diagnosis and surgical intervention are crucial for managing complex congenital conditions like Pentalogy of Cantrell with cardiac diverticulum.
  • Cardiovascular imaging plays a vital role in guiding treatment decisions for these rare pediatric cases.

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