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A Gastroenterologist's Guide to Care Transitions in Cystic Fibrosis from Pediatrics to Adult Care
Dhiren Patel1,2, Michelle Baliss3, Pavithra Saikumar1
1Department of Pediatrics, Division of Pediatric Gastroenterology, Hepatology and Nutrition, Cardinal Glennon Children's Medical Center, Saint Louis University School of Medicine, St. Louis, MO 63104, USA.
Insights
Cystic Fibrosis (CF) impacts the GI tract throughout life. This review highlights key GI care needs during patient transition and offers a checklist for smoother care coordination.
Area of Science:
- Gastroenterology
- Pediatrics
- Pulmonology
Background:
- Cystic Fibrosis (CF) is a multi-system chronic illness with significant gastrointestinal (GI) manifestations.
- GI care in CF is crucial for overall health, impacting morbidity, lung function, and quality of life for patients with CF (PwCF).
- Patient care needs evolve from infancy through adulthood, necessitating specialized management strategies.
Purpose of the Study:
- To review essential gastrointestinal care considerations during the transition of pediatric to adult care for PwCF.
- To identify challenges faced by patients and providers during this critical care phase.
- To introduce a practical checklist to facilitate effective GI care transition in CF.
Main Methods:
- Literature review focusing on GI manifestations and management in pediatric and adult CF patients.
- Analysis of current care transition processes and identified gaps.
- Development of a transition checklist based on best practices in CF gastrointestinal care.
Main Results:
- GI symptoms and management complexities in CF vary significantly across pediatric and adult populations.
- The transition from pediatric to adult care presents unique challenges for GI management continuity.
- A structured checklist can aid in standardizing and improving the GI care transition process.
Conclusions:
- Effective GI care transition is vital for PwCF, requiring coordinated efforts between pediatric and adult healthcare teams.
- The proposed checklist addresses critical GI aspects, aiming to improve management continuity and patient outcomes.
- Further development and implementation of transition tools are needed to support GI providers and PwCF.
Abstract:
Cystic Fibrosis is a chronic disease affecting multiple systems, including the GI tract. Clinical manifestation in patients can start as early as infancy and vary across different age groups. With the advent of new, highly effective modulators, the life expectancy of PwCF has improved significantly. Various GI aspects of CF care, such as nutrition, are linked to an overall improvement in morbidity, lung function and the quality of life of PwCF. The variable clinical presentations and management of GI diseases in pediatrics and adults with CF should be recognized. Therefore, it is necessary to ensure efficient transfer of information between pediatric and adult providers for proper continuity of management and coordination of care at the time of transition. The transition of care is a challenging process for both patients and providers and currently there are no specific tools for GI providers to help ensure a smooth transition. In this review, we aim to highlight the crucial features of GI care at the time of transition and provide a checklist that can assist in ensuring an effective transition and ease the challenges associated with it.
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