A Gastroenterologist's Guide to Care Transitions in Cystic Fibrosis from Pediatrics to Adult Care

Dhiren Patel1,2, Michelle Baliss3, Pavithra Saikumar1

  • 1Department of Pediatrics, Division of Pediatric Gastroenterology, Hepatology and Nutrition, Cardinal Glennon Children's Medical Center, Saint Louis University School of Medicine, St. Louis, MO 63104, USA.

Insights

Cystic Fibrosis (CF) impacts the GI tract throughout life. This review highlights key GI care needs during patient transition and offers a checklist for smoother care coordination.

Area of Science:

  • Gastroenterology
  • Pediatrics
  • Pulmonology

Background:

  • Cystic Fibrosis (CF) is a multi-system chronic illness with significant gastrointestinal (GI) manifestations.
  • GI care in CF is crucial for overall health, impacting morbidity, lung function, and quality of life for patients with CF (PwCF).
  • Patient care needs evolve from infancy through adulthood, necessitating specialized management strategies.

Purpose of the Study:

  • To review essential gastrointestinal care considerations during the transition of pediatric to adult care for PwCF.
  • To identify challenges faced by patients and providers during this critical care phase.
  • To introduce a practical checklist to facilitate effective GI care transition in CF.

Main Methods:

  • Literature review focusing on GI manifestations and management in pediatric and adult CF patients.
  • Analysis of current care transition processes and identified gaps.
  • Development of a transition checklist based on best practices in CF gastrointestinal care.

Main Results:

  • GI symptoms and management complexities in CF vary significantly across pediatric and adult populations.
  • The transition from pediatric to adult care presents unique challenges for GI management continuity.
  • A structured checklist can aid in standardizing and improving the GI care transition process.

Conclusions:

  • Effective GI care transition is vital for PwCF, requiring coordinated efforts between pediatric and adult healthcare teams.
  • The proposed checklist addresses critical GI aspects, aiming to improve management continuity and patient outcomes.
  • Further development and implementation of transition tools are needed to support GI providers and PwCF.

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