Rectal Bleed in a Child With Abernathy Malformation- Endovascular Management

Area of Science:

• Vascular Surgery
• Interventional Radiology
• Hepatology

Background:

• Abernathy malformations are congenital extrahepatic portosystemic shunts diverting portal blood away from the liver.
• These shunts can lead to metabolic derangements like hyperammonemia and hepatic encephalopathy, as well as anatomical issues such as varices.
• Interventional radiology is crucial for diagnosis and minimally invasive management of these conditions.

Observation:

• A rare case of a peripheral congenital portosystemic shunt was observed.
• The shunt connected the inferior mesenteric vein to the internal iliac vein.
• The patient presented with rectal bleeding.

Findings:

• The case highlights a unique anatomical variation of Abernathy malformation.
• Diagnostic and therapeutic interventions were successfully performed within the interventional radiology department.
• A holistic, minimally invasive approach was employed.

Implications:

• This case underscores the importance of interventional radiology in managing rare vascular anomalies.
• Minimally invasive techniques can reduce procedure time and hospital stays.
• Early diagnosis and management are key to preventing severe complications associated with portosystemic shunts.