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Nonfunctioning adrenocortical carcinoma in a young girl
The Japanese Journal of Surgery
|November 1, 1985
Summary
Adrenocortical carcinoma, a rare adrenal cancer, was diagnosed in a 9-year-old girl. Despite surgical removal, the cancer recurred, leading to metastasis and death.
Area of Science:
- Pediatric Oncology
- Surgical Pathology
Background:
- Adrenocortical carcinoma is a rare malignancy originating from the adrenal cortex.
- Pediatric cases are exceptionally uncommon and often present with distinct clinical features.
Observation:
- A 9-year-old girl presented with left hypochondrial pain and a palpable abdominal mass.
- Imaging revealed a large tumor compressing the left kidney.
- No hormonal abnormalities were detected clinically or biochemically.
Findings:
- Pathological examination confirmed adrenocortical carcinoma.
- The tumor was surgically excised along with the left kidney.
- Postoperative adjuvant therapy (radiotherapy or chemotherapy) was not administered.
Implications:
- The case highlights the aggressive nature of pediatric adrenocortical carcinoma.
- Metastasis to the liver and local recurrence occurred within 40 months post-surgery.
- This underscores the need for vigilant long-term follow-up in pediatric adrenocortical carcinoma survivors.