Biventricular Arrhythmogenic Cardiomyopathy Mimicking Cardiac Sarcoidosis
Mouna Kodali1, Patrycja Galazka1,2, Asad Ghafoor1,2
1Aurora Cardiovascular and Thoracic Services, Aurora Sinai/Aurora St. Luke's Medical Centers, Milwaukee, Wisconsin, USA.
JACC. Case Reports
|February 21, 2024
Abstract:
Noninvasive imaging is crucial for diagnosing and managing arrhythmogenic cardiomyopathy. Despite advanced multimodality imaging tools, challenges persist in differentiating it from other arrhythmogenic diseases (eg, cardiac sarcoidosis). We present a case of arrhythmogenic cardiomyopathy with an FLNC variant of uncertain significance exhibiting a phenocopy of cardiac sarcoidosis.


