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Complicated type B aortic dissection in a pregnant woman with Marfan syndrome

Mohammad M Zagzoog1,2, Sean A Crawford3, Jean-Michel Davaine1,2

  • 1Department of Vascular and Endovascular Surgery, Pitié-Salpetriere University Hospital, Sorbonne Université, Faculty of Medicine, Paris, France.

Journal of Vascular Surgery Cases and Innovative Techniques
|August 27, 2024
PubMed

Marfan syndrome is a rare inherited connective tissue disorder that can result in significant morbidity and mortality. We report a case of a 29-year-old pregnant woman presenting with an acute type B aortic dissection. Owing to cardiopulmonary decompensation and intestinal malperfusion, she underwent an emergency cesarean section followed by left subclavian to carotid transposition and thoracic endovascular aortic repair that was complicated by a retrograde type A aortic dissection and was managed surgically. Molecular testing confirmed the diagnosis of Marfan syndrome. This case highlights that multidisciplinary and hybrid management of challenging cases of acute aortic syndromes can result in a favorable outcome.

Keywords:
Aortic dissectionMarfan syndromePregnancyRetrograde type A aortic dissectionThoracic endovascular aortic repair

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