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Systemic Amyloidosis Presenting as Budd-Chiari Syndrome: A Case Report
Naman Lodha1, Samarth Bhat K S1, Kartikeya Mathur2
1Department of General Medicine, All India Institute of Medical Sciences, Jodhpur, Rajasthan, India.
Middle East Journal of Digestive Diseases
|October 10, 2024
Summary
Systemic amyloidosis, a protein misfolding disorder, can rarely manifest as Budd-Chiari syndrome (BCS), a liver vein obstruction. This case highlights the importance of considering amyloid light chain amyloidosis in BCS diagnosis.
Area of Science:
- Hepatology
- Nephrology
- Cardiology
- Hematology
Background:
- Budd-Chiari syndrome (BCS) involves hepatic venous outflow obstruction, often linked to hypercoagulable states.
- Systemic amyloidosis is characterized by misfolded protein deposition causing end-organ damage and coagulation abnormalities.
- Amyloidosis frequently presents with bleeding diathesis, complicating its clinical picture.
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