Myoepithelial Carcinoma of the External Auditory Canal With Extension Into the Middle Ear and Mastoid

Myoepithelial carcinoma is a rare disease of the head and neck, with only a handful of cases reported occurring within the external auditory canal, middle ear, and mastoid. The patient discussed is a 67-year-old male with a prior history of a bilateral tympanomastoidectomy for cholesteatoma and a prior history of left parotidectomy and adjuvant radiation for pleomorphic sarcoma. Three years after the parotidectomy, the patient presented with contralateral ear fullness. During an intraoperative examination, a fibrous mass was encountered, which revealed an invasive salivary gland neoplasm, myoepithelial subtype. Definitive treatment consisted of a right radical mastoidectomy, temporal bone resection, and canal closure with adjuvant chemoradiation. This case serves to contribute to the established literature regarding this particular subtype of head and neck cancer, as well as provide the reader with a brief review of this rare entity.