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Bilateral Pulmonary Arteriovenous Malformations: Challenges in a Rare and Complex Case

Aayushi Joshi1, Vasu Saini1, Bhumika Bheemavarapu2

  • 1Pediatrics, Shri Guru Ram Rai Institute of Medical and Health Sciences, Dehradun, IND.

Cureus
|October 28, 2024
PubMed

Insights

Pulmonary arteriovenous malformations (PAVMs) can cause cyanosis in children. Endovascular treatment effectively closed multiple PAVMs in a young boy, resolving his symptoms.

Area of Science:

  • Vascular Surgery
  • Pediatric Cardiology
  • Interventional Radiology

Background:

  • Pulmonary arteriovenous malformations (PAVMs) are rare vascular anomalies connecting pulmonary arteries and veins.
  • PAVMs can lead to severe complications like paradoxical emboli, necessitating timely diagnosis and management in children.

Observation:

  • A five-year-old boy presented with persistent cyanosis and clubbing over eight months.
  • Imaging and angiography identified multiple, diffuse, bilateral PAVMs.

Findings:

  • The patient's PAVMs were successfully treated using an endovascular approach.
  • This intervention aimed to eliminate the abnormal vascular connections.

Implications:

  • Endovascular treatment is a viable option for complex PAVMs in pediatric patients.
  • Prompt management of PAVMs can prevent life-threatening embolic events and improve cyanosis.

Keywords:
congenital abnormalitiescongenital birth defectcongenital diseaseendovascular coil embolizationhereditary hemorrhagic telangiectasia (hht)pavmperioral cyanosispulmonary arteriovenous malformations

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