Reticulate pigmented anomaly of the flexures associating reticulate acropigmentation: one single entity

We describe a patient and her family in whom the clinical features of reticulate pigmented anomaly of the flexures, also known as Dowling-Degos disease, are associated with those of Kitamura's reticulate acropigmentation. This family is the second in which the concurrence of such rare genodermatoses is reported. It seems likely that Dowling-Degos disease, and Kitamura's reticulate acropigmentation are different clinical expressions of the same entity.