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Congenital Infantile Fibrosarcoma - A Potentially Fatal Condition.
Bipin Arun Ghanghurde1, Kushal Shah1, Minnie Bodhanwala1
1Bai Jerbai Wadia Hospital for Children, Mumbai, Maharashtra, India.
Congenital infantile fibrosarcoma (CIF) is a rare infant tumor. Early diagnosis and treatment, including amputation in severe cases like DIC, are vital for limb and life preservation.
Area of Science:
- Pediatric Oncology
- Surgical Oncology
- Dermatopathology
Background:
- Congenital infantile fibrosarcoma (CIF) is a rare malignant tumor in infants.
- CIF can be misdiagnosed as vascular malformations or hemangiomas.
- Timely diagnosis and intervention are critical for patient outcomes.
Observation:
- A 4-month-old infant presented with CIF of the left forearm and arm.
- The tumor manifested as a swelling with a bleeding ulcer.
- The infant developed disseminated intravascular coagulation (DIC) during hospitalization.
Findings:
- The case highlights the aggressive nature of CIF.
- Disseminated intravascular coagulation (DIC) is a severe complication of CIF.
- Prompt surgical intervention, including amputation, may be life-saving.
Implications:
- This case underscores the importance of considering CIF in infant limb swellings.
- Aggressive management, including amputation, may be necessary for CIF with complications.
- Further research into CIF diagnosis and treatment is warranted.
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