Pulmonary Atresia Intact Ventricular Septum With Anomalous Left Coronary Artery From Pulmonary Artery
Kalpana Singh Norbisrath1, Sonia Labarinas1, Jon Meliones1
1Children's Heart Institute, Children's Memorial Hermann Hospital, Houston, Texas.
Abstract:
A patient with known pulmonary atresia and intact ventricular septum and ductal stent presented with low cardiac output and arrythmia. Intraoperatively, the patient was found to have an anomalous left coronary artery arising from the pulmonary artery. After reimplantation of the left coronary artery to the aortic root and placement of a central shunt, the patient progressed well and was discharged home. A high index of suspicion and clear diagnostic visualization of both right and left coronary artery origins are needed to diagnose this highly fatal yet treatable lesion properly.
Related Concept Videos
Coronary Circulation
Coronary circulation begins at the base of the aorta, where two main arteries arise—the left and right coronary arteries. These arteries encircle the heart in the coronary sulcus and supply the...
Overview of Pulmonary Circulation
The process begins with the right ventricle of the heart pumping deoxygenated blood into the pulmonary trunk. This large vessel extends about 5 centimeters before splitting into the left and right pulmonary arteries. These arteries...
Overview of Systemic and Pulmonary Circulation
The oxygenated blood is sent...
Chambers of the Heart
Deoxygenated blood from the body is received in the right...
Fetal Circulation
Two umbilical arteries transport blood from the fetus to the placenta. At the placenta, the blood absorbs oxygen and nutrients while simultaneously eliminating waste products. This oxygen-enriched and nutrient-rich blood then returns to the fetus through one...
Cardiovascular System Abnormal Findings II: Auscultation
Abnormal Heart Sounds
Gallops:


