Sequential Double-Lung Transplantation In Kartagener Syndrome: A Case Report.

Area of Science:

• Cardiology
• Pulmonology
• Surgical Innovation

Background:

• Kartagener syndrome (KS) presents unique anatomical challenges for lung transplantation, including dextrocardia and altered hilar structures.
• End-stage lung failure necessitates advanced treatment options, with lung transplantation being a critical intervention.

Purpose of the Study:

• To describe a successful double-lung transplant in a patient with Kartagener syndrome.
• To demonstrate the feasibility of lung transplantation without extracorporeal oxygenation in complex KS anatomy.

Main Methods:

• A 48-year-old male patient with KS underwent a double-lung transplant using a Clamshell incision.
• Surgical technique involved preserving longer donor pulmonary arteries and right main bronchus for anastomosis.
• The procedure was performed without extracorporeal circulation or complex plastic maneuvers.

Main Results:

• The lung transplant was successfully completed without complications.
• The patient was discharged 32 days post-surgery.
• Anatomical adaptations allowed for end-to-end arterial and bronchial anastomosis, avoiding unnecessary procedures like right inferior lobe wedge resection.

Conclusions:

• Lung transplantation can be successfully performed in patients with Kartagener syndrome despite anatomical complexities.
• The absence of extracorporeal oxygenation demonstrates a potentially less invasive approach.
• This case supports lung transplantation as a viable treatment for end-stage lung disease in KS patients.