Congenital simple hamartoma of the retinal pigment epithelium. About three cases
A B González Escobar1, M A López-Egea Bueno1, A González Gómez1
1Departamento de Oftalmología del Hospital Virgen de la Victoria, Málaga, Spain.
Abstract:
Congenital simple hamartoma of the retinal pigment epithelium (CSHRPE) is a very rare benign tumor (usually diagnosed in a routine fundus examination), which presents as a small, pigmented nodular lesion in the macular area. We present 3 clinical cases of CSHRPE located in the macular region observed casually and diagnosed thanks to autofluorescence and especially optical coherence tomography, non-invasive tests. We want to point out the importance of carrying out the differential diagnosis of this lesion, especially with malignant tumors, to avoid unnecessary procedures and the importance of following up, since they are usually asymptomatic but are sometimes associated with complications such as traction and exudation.
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