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An ACTH-Producing Neuroendocrine Tumor: Clinical Course of Multidisciplinary Therapy Including Peptide Receptor
Tomonobu Koizumi1, Ai Sato2, Kohei Kitajima2
1Shinshu Cancer Center, Shinshu University Hospital, Matsumoto, Japan.
Case Reports in Oncology
|February 21, 2025
Summary
Peptide receptor radionuclide therapy (PRRT) effectively treated a rare adrenocorticotropic hormone (ACTH)-producing neuroendocrine tumor (NET). Careful management is crucial to address potential hormonal crises during PRRT for these complex NETs.
Area of Science:
- Endocrinology
- Oncology
- Nuclear Medicine
Background:
- Adrenocorticotropic hormone (ACTH)-producing neuroendocrine tumors (NETs) are rare, presenting complex clinical challenges.
- Ectopic ACTH production leads to Cushing's syndrome, requiring multifaceted treatment strategies.

