[Lymphangioleiomyomatosis of the retroperitoneal space]

The clinical course and the results of histological examination of retroperitoneal lymphangioleiomyomatosis in a woman of 32 are presented. The main morphological features of the disease were as follows: localization of tumour cells around the vascular spaces, accumulation of mature lymphocytes in the vascular spaces and among tumour cells, pronounced argyrophilic carcass of the tumour.