Susac Syndrome with Classical Triad: A Case Report and Literature Review

Susac syndrome is a rare microangiopathy affecting the brain, retina, and cochlea. Individuals affected typically present with a classical clinical triad of branch retinal artery occlusion (BRAO), encephalopathy or white matter lesions, and sensorineural hearing loss. Herein, we report an exceedingly rare case of a middle-aged female patient with multiple presentations related to her visual field complaints. The presence of multiple bilateral BRAOs, in addition to sensorineural hearing impairment and white matter lesions on the brain magnetic resonance imaging, led to the diagnosis of Susac syndrome. Cases of Susac syndrome are few and far between and have seldom been reported in detail. Awareness of this rare presentation by clinicians and radiologists is of utmost importance to aid in correctly diagnosing and treating such patients.