Inflammatory Linear Verrucous Epidermal Nevus (ILVEN): A Scarce Cognate with a Neoplasia

Inflammatory linear verrucous epidermal nevus (ILVEN) is a rare type of cutaneous nevus that has female predilection which occurs at birth or infancy and evolves along Blaschko's lines, perceived unilaterally, over the buttocks, legs, and arms. In this case report, ILVEN was associated with multiple ulcero-proliferative skin lesions over the dorsum of the left foot, which on biopsy were proven to be malignant adnexal tumors. A 51-year-old female presented with linear, scaly, and verrucous skin lesions on her left buttock, thigh, and leg unilaterally along Blaschko's lines after birth. Post-operative biopsy taken from the dorsum of the foot reveals trichoepithelioma. Biopsy taken from the back of the thigh and leg reveals inflammatory linear verrucous epidermal nevus. Single-stage surgical resection of both lesions, performed with primary closure of all the areas, except the gluteal region which is closed by V-Y advancement flap. The outcome was satisfactory for the patient after surgical resection and reconstruction. No recurrence was detected during the follow-up visits. ILVEN is an uncommon type of hyperplastic cutaneous disease. ILVEN perchance associated with malignancy. Henceforth, it has to be considered during the evaluation of similar lesions for optimal treatment intervention.