Right-sided partial anomalous pulmonary venous connection with intact atrial septum and small left atrium: in a...

Partial anomalous pulmonary venous connection (PAPVC) is a rare congenital heart defect (CHD), with reported incidence between 0.4 and 0.7%. PAPVC with intact atrial septum (IAS) is extremely uncommon, and associated small left atrium (LA) with dilated coronary sinus (CS) is even rarer. We present a case of isolated right-sided PAPVC draining into the right atrium (RA) with bilateral superior vena cavae (SVC) and an intact interatrial septum with dilated coronary sinus and a small diminutive LA, in a dextroverted heart. The patient underwent PAPVC rerouting and LA augmentation via biatrial appendage approaches, through median sternotomy. The patient recovered uneventfully and is doing well on 1-month follow-up.