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Updated: Jul 6, 2026
10:21
Scanning Electron Microscopy of Macerated Tissue to Visualize the Extracellular Matrix
Published on: June 14, 2016
Accessory Mitral Valve Tissue in Both Obstructive and Nonobstructive Hypertrophic Cardiomyopathy Cases
İrem Türkmen1, Arda Güler1, Sezgin Atmaca1
1Department of Cardiology, University of Health Sciences, Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Training and Research Hospital, Istanbul, Turkiye.
Summary
Accessory mitral valve tissue (AMVT) is a rare congenital heart anomaly. Its adult diagnosis alongside hypertrophic cardiomyopathy (HCM) is exceptionally rare, complicating diagnosis and requiring advanced imaging.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Cardiac Imaging
Background:
- Accessory mitral valve tissue (AMVT) is a rare congenital cardiac anomaly.
- It is typically diagnosed in childhood, with adult presentation being exceptionally rare.
- Coexistence with hypertrophic cardiomyopathy (HCM) is particularly uncommon.
Observation:
- This case series focuses on adult patients with hypertrophic cardiomyopathy (HCM).
- The study observed the complex diagnostic challenges posed by coexisting AMVT and HCM.
- Left ventricular outflow tract (LVOT) gradient formation was a key diagnostic consideration.
Findings:
- Multimodal imaging is crucial for accurate identification of AMVT in adults with HCM.
- Differentiating AMVT from other cardiac conditions is essential for proper management.
- Various morphologies of AMVT were identified, impacting diagnostic and therapeutic strategies.
Implications:
- Highlights the importance of considering rare congenital anomalies like AMVT in adult cardiology.
- Emphasizes the role of advanced imaging techniques in diagnosing complex cardiac conditions.
- Informs clinical practice regarding the evaluation and management of patients with coexisting HCM and AMVT.
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