Acute Angioid Streak Retinopathy is a Two-Phase Inflammatory Process Starting with Outer Retinal Inflammation,

Sara Touhami1, Sabrina Rigo1, Emilien Faudi1

  • 1Ophthalmology Department, Sorbonne Université, Pitié-Salpêtrière University Hospital, Paris, France.

Summary

Recurrent acute angioid streak retinopathy (AASR) in a pseudoxanthoma elasticum patient involves a two-phase inflammatory process. Initial RPE/BM disruption at angioid streaks leads to inflammation, followed by secondary multiple evanescent white dot syndrome (MEWDS).