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Updated: Sep 17, 2025

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Three-Dimensional Printing of a Complex Aortic Anomaly
Published on: November 1, 2018
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Using Multimodality Imaging and 3-Dimensional Printed Models to Guide Decision-Making for Complex Congenital
Sukran Erdem1, Munes Fares1, Felipe Murguia1
1Division of Pediatric Cardiology, Department of Pediatrics, The University of Texas Southwestern Medical Center, Dallas, Texas, USA.
JACC. Case Reports
|June 27, 2025
Summary
Advanced 3D modeling and multimodality imaging, including cardiac MRI, enhance surgical planning for complex congenital heart disease (CHD). This approach improves anatomical visualization and guides complex staged cardiac repairs for better patient outcomes.
Area of Science:
- Cardiology
- Medical Imaging
- Pediatric Surgery
Background:
- Conventional 2D echocardiography and cross-sectional imaging pose challenges in surgical planning for complex congenital heart disease (CHD).
- Accurate anatomical assessment is crucial for determining optimal surgical strategies in CHD patients.
Observation:
- An 11-month-old patient with heterotaxy syndrome, dextrocardia, double-outlet right ventricle, and pulmonary valve stenosis presented with complex cardiac anatomy.
- Multidisciplinary discussion was essential for planning a staged cardiac repair due to the intricate nature of the condition.
Findings:
- Three-dimensional (3D) printed and virtual heart models, alongside CMR angiography, offered detailed visualization and spatial understanding.
- These advanced imaging techniques facilitated assessment of a staged biventricular repair's feasibility.
- Postoperative CMR was instrumental in guiding subsequent surgeries, evaluating repair structures, and identifying complications.
Implications:
- Multimodality imaging, particularly advanced techniques like 3D modeling, plays a critical role in surgical planning for complex CHD.
- Enhanced visualization and spatial conceptualization improve the precision and success rates of complex cardiac surgeries.
- This case underscores the value of integrating novel imaging modalities into the management of pediatric congenital heart defects.
Keywords:
3-dimensional printingcardiac magnetic resonancecomputed tomographycongenital heart defectdouble-outlet right ventricleechocardiography
