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Right Ventricular Outflow Conduit Stenosis After Childhood Ross-Konno Procedure
Lakshmi Kattamuri1, Kunal Sharma1, Kahtan Fadah2
1Department of Internal Medicine, Texas Tech University Health Sciences Center, El Paso, Texas, USA.
Right ventricle-pulmonary artery (RV-PA) conduit stenosis, a complication of childhood surgery, requires surgical conduit replacement in adults. Multimodal imaging aids in assessing complex congenital heart disease.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Cardiac Surgery
Background:
- Right ventricle-pulmonary artery (RV-PA) conduit stenosis is an uncommon complication following childhood Ross-Konno procedures.
- Adults with congenital heart disease may present with late-onset complications from prior surgical interventions.
Observation:
- A young adult presented with progressive dyspnea due to severe RV-PA conduit stenosis.
- Diagnostic workup included echocardiography, cardiac CT, and right heart catheterization, revealing significant obstruction and pulmonary hypertension.
Findings:
- Multimodal imaging confirmed severe, calcified RV-PA conduit stenosis.
- The patient exhibited reduced left ventricular ejection fraction and severe pulmonary hypertension secondary to the obstruction.
Implications:
- Surgical conduit replacement is the definitive treatment for small, calcified RV-PA conduits.
- Comprehensive imaging assessment is crucial for guiding interventions in adults with complex congenital heart disease.
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