Naevoid basal-cell carcinoma syndrome with unilateral neoplasms and pits

A patient with the naevoid basal-cell carcinoma syndrome (NBCCS) is reported in whom non-aggressive neoplasms developed predominantly on the right side of the body. It is proposed that a post-zygotic somatic mutation is most likely to be responsible for the unilateral manifestation of the syndrome in this patient.