Conus Branch Fistula to Main Pulmonary Artery: A Rare Coronary Anomaly that May Cause Chest Pain in a Pediatric

Leila Bigdelu1, Ossama Maadarani2, Ali Azari1

  • 1Vascular and Endovascular Surgery Research Center, Mashhad University of Medical Sciences, Mashhad, Iran.

Insights

Coronary artery fistulas (CAFs) are rare heart conditions. This case highlights a unique CAF variant in a child presenting with chest pain, emphasizing the need for thorough diagnosis.

Area of Science:

  • Cardiology
  • Pediatric Cardiology
  • Congenital Heart Disease

Background:

  • Coronary artery fistulas (CAFs) are uncommon congenital abnormalities.
  • They represent abnormal connections between coronary arteries and cardiac chambers or great vessels.
  • While often congenital, iatrogenic causes are increasing due to medical interventions and trauma.

Purpose of the Study:

  • To report a rare variant of coronary artery fistula in a pediatric patient.
  • To discuss the diagnostic approach and clinical presentation of CAFs in children.
  • To highlight potential causes of chest pain in pediatric cardiology.

Main Methods:

  • Case report of an 11-year-old boy with atypical chest pain.
  • Diagnostic workup included cardiac imaging (details not specified in abstract).
  • Review of literature on coronary artery fistulas in pediatric populations.

Main Results:

  • The patient was diagnosed with a rare variant of coronary artery fistula.
  • The condition did not result in significant hemodynamic complications in this case.
  • The patient presented with atypical chest pain, a potential symptom of CAF.

Conclusions:

  • Coronary artery fistula is a rare anomaly, often found incidentally.
  • Diagnostic tools like echocardiography, CT coronary angiography, MRI, and conventional angiography are crucial for visualization and hemodynamic assessment.
  • A fistula between a conus branch and the pulmonary artery is a rare pediatric variation that can cause chest pain.

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