A Rare Case of Shone Complex With a Persistent Left Superior Vena Cava and Absent Right Superior Vena Cava

Balaji Aironi1, Gaurish Sawant1,2, Palakkumar P Shah1

  • 1Cardiovascular and Thoracic Surgery, King Edward Memorial Hospital and Seth Gordhandas Sunderdas Medical College, Mumbai, IND.

Cureus
|July 11, 2025
PubMed

Insights

Shone complex, a rare congenital heart defect, involves left heart obstructions. This case highlights an incomplete form with associated anomalies, emphasizing the need for thorough diagnosis and surgical planning.

Area of Science:

  • Cardiology
  • Pediatric Cardiology
  • Congenital Heart Disease

Background:

  • Shone complex is a rare congenital heart disease characterized by multiple left-sided obstructive lesions.
  • It is often underdiagnosed due to its rarity and complex presentation.

Observation:

  • This report details a rare case of incomplete Shone complex.
  • The patient presented with additional associated anomalies, complicating the clinical picture.

Findings:

  • Accurate diagnosis of incomplete Shone complex requires an extensive clinical workup.
  • Associated anomalies necessitate a comprehensive evaluation for appropriate management.

Implications:

  • Early and accurate diagnosis is crucial for effective surgical planning in Shone complex.
  • Understanding associated anomalies improves patient outcomes and treatment strategies.

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