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Endomyocarditis in Eosinophilic Granulomatosis With Polyangiitis: Cardiac Magnetic Resonance Imaging Highlights
Eduardo Pereyra Acha1, David López Gómez2, Cristina Moure Roget1
1Department of Cardiology, Consorci Sanitari de Terrassa-Hospital Universitari, Terrassa, Barcelona, Spain.
Background:
Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare vasculitis; cardiac involvement is common and worsens prognosis.
Case Summary:
A 42-year-old man presented with chest pain, marked ST-T changes, eosinophilia, and elevated troponin, without obstructive coronary disease. He was diagnosed with acute eosinophilic endomyocarditis, mildly reduced left ventricular (LV) ejection fraction, and a large apical thrombus-an initial manifestation of probable EGPA. The patient received anticoagulation, corticosteroids, and immunosuppressive therapy. Endomyocardial fibrosis was confirmed via LV biopsy. During follow-up, electrocardiography and troponin T normalized, cardiac magnetic resonance (CMR) showed thrombus resolution, LV function recovery, and persistent subendocardial fibrosis.
Discussion:
This case illustrates severe cardiac involvement in EGPA, with serial cardiac testing including striking electrocardiogram and CMR findings.
Take-Home Message:
Cardiac involvement in EGPA is prevalent. Complete cardiac screening including CMR is advisable in all patients.
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