Fronto-orbito-sphenoidal fibrous dysplasia

Area of Science:

• Neurosurgery
• Ophthalmology
• Craniofacial Surgery

Background:

• Fronto-orbito-sphenoidal fibrous dysplasia presents with cosmetic deformities and potential vision loss.
• Proptosis and optic canal narrowing are significant complications impacting visual function.

Purpose of the Study:

• To evaluate the efficacy of surgical excision and autogenous bone grafting for fronto-orbito-sphenoidal fibrous dysplasia.
• To assess the role of optic nerve decompression in preserving or improving vision.

Main Methods:

• Radical or near-radical excision of affected bone.
• Immediate reconstruction using autogenous bone grafts.
• Optic nerve decompression in cases with narrowed optic canals.

Main Results:

• Successful cosmetic improvement in all eight patients.
• Halting of visual loss progression post-surgery.
• Vision improvement in one eye following optic nerve decompression; no change in other eyes.

Conclusions:

• Surgical management offers significant cosmetic and functional benefits for fronto-orbito-sphenoidal fibrous dysplasia.
• Autogenous bone grafting provides effective reconstruction.
• Optic nerve decompression is a valuable adjunct for preventing further visual deterioration.