Search research articles

ABOUT JoVE

Overview Leadership Blog JoVE Help Center

AUTHORS

Publishing Process Editorial Board Scope & Policies Peer Review FAQ Submit

LIBRARIANS

Testimonials Subscriptions Access Resources Library Advisory Board FAQ

RESEARCH

JoVE Journal Methods Collections JoVE Encyclopedia of Experiments Archive

EDUCATION

JoVE Core JoVE Business JoVE Science Education JoVE Lab Manual Faculty Resource Center Faculty Site

Terms & Conditions of Use

Related Concept Videos

Cystic Fibrosis: Management

Cystic Fibrosis: Management

Cystic fibrosis (CF) is an autosomal recessive disorder that predominantly affects individuals of Northern European descent, occurring at a rate of 1 in 3500. It is caused by a genetic mutation in a gene on chromosome 7, most commonly the ΔF508 mutation, that codes for the cystic fibrosis transmembrane conductance regulator (CFTR) protein. This results in thicker mucus secretions and obstruction pathologies in multiple organs, including the lungs and sinuses.
Sinus disease and chronic...

You might also read

Related Articles

Articles linked to this work by shared authors, journal, and citation graph.

Sort by

Same author

<i>Pseudomonas aeruginosa</i> infection causes lysosomal dysfunction in the cystic fibrosis bronchial epithelium.

Infection and immunity·2026

Same author

Daily Routines and Habits in Individuals with Attention Deficit Hyperactivity Disorder: A Scoping Review.

Behavioral sciences (Basel, Switzerland)·2026

Same author

Sex differences in cardiovascular disease risk in type 1 diabetes: The vascular bed paradox in women.

Diabetes & vascular disease research·2026

Same author

Sex, Race and Ethnicity, and Rurality Disparities in Cardiovascular Death Among Adults With Early-Onset Colorectal Cancer: A Retrospective Cohort Analysis.

Journal of the American Heart Association·2026

Same author

Pilot and Feasibility Study of an Individualized Telehealth Exercise Program for People with Cystic Fibrosis.

Journal of functional morphology and kinesiology·2026

Same author

Racial disparity in microvascular function among non-Hispanic white and non-Hispanic black men with newly diagnosed prostate cancer.

Physiological reports·2026

Search research articles

Related Experiment Video

Updated: Sep 8, 2025

Home-Based Prescribed Pulmonary Exercise in Patients with Stable Chronic Obstructive Pulmonary Disease

Home-Based Prescribed Pulmonary Exercise in Patients with Stable Chronic Obstructive Pulmonary Disease

Published on: August 24, 2019

Survey Validation of Exercise and Body Composition Testing and Exercise Training Programs for People With Cystic

Najlaa Z Alotaibi^1,2, Donald H Lein^1,3, Hon K Yuen^1,4

¹Rehabilitation Science PhD Program, University of Alabama at Birmingham, Birmingham, Alabama, USA.

Pediatric Pulmonology

|September 5, 2025

Summary

This study developed and validated a survey to assess exercise and body composition testing in cystic fibrosis (CF) care centers. The validated survey will help identify barriers and facilitators to implementing these crucial assessments for people with CF.

Keywords:

Delphi survey body composition cystic fibrosis exercise testing exercise training

More Related Videos

A Novel Digital Platform for a Monitored Home-based Cardiac Rehabilitation Program

A Novel Digital Platform for a Monitored Home-based Cardiac Rehabilitation Program

Published on: April 19, 2019

Author Spotlight: Implementation of BIVA for Analyzing Disease Risk Factors in Patients with Low Body Cell Mass

Author Spotlight: Implementation of BIVA for Analyzing Disease Risk Factors in Patients with Low Body Cell Mass

Published on: July 14, 2023

Related Experiment Videos

Last Updated: Sep 8, 2025

Home-Based Prescribed Pulmonary Exercise in Patients with Stable Chronic Obstructive Pulmonary Disease

Home-Based Prescribed Pulmonary Exercise in Patients with Stable Chronic Obstructive Pulmonary Disease

Published on: August 24, 2019

A Novel Digital Platform for a Monitored Home-based Cardiac Rehabilitation Program

A Novel Digital Platform for a Monitored Home-based Cardiac Rehabilitation Program

Published on: April 19, 2019

Author Spotlight: Implementation of BIVA for Analyzing Disease Risk Factors in Patients with Low Body Cell Mass

Author Spotlight: Implementation of BIVA for Analyzing Disease Risk Factors in Patients with Low Body Cell Mass

Published on: July 14, 2023

Area of Science:

Pulmonary Medicine
Exercise Physiology
Clinical Research

Background:

Exercise and body composition assessments are vital for managing cystic fibrosis (CF).
Current CF care guidelines recommend exercise testing and counseling.
Underutilization of these assessments in CF care centers necessitates further investigation.

Purpose of the Study:

To develop and validate a comprehensive survey instrument.
To explore barriers and facilitators to exercise and body composition testing in CF care.
To inform strategies for improving assessment utilization in CF care.

Main Methods:

A Delphi methodology was employed with 79 invited experts in exercise and CF.
Expert feedback was gathered over three rounds to refine a survey instrument.
A final 114-item survey was validated based on expert consensus.

Main Results:

Thirteen subject matter experts participated, with six completing all three rounds.
The survey underwent significant revision, with 46 items retained, 58 revised, 2 dropped, and 8 added.
A validated 114-item survey was established for use in CF care centers.

Conclusions:

A validated survey instrument is now available for CF care centers.
The survey will provide insights into the benefits and barriers of key assessments.
Findings will support improved implementation of exercise and body composition testing for people with CF, especially in the era of CFTR modulators.