A Case of a Solitary Angiokeratoma Circumscriptum of the Lower Leg

Angiokeratoma circumscriptum (AKC) is a rare congenital vascular malformation that often mimics other skin conditions such as verrucous venous malformation. We report a case of AKC in a 9-year-old male presenting with a pruritic, hyperkeratotic lesion growing proportionally to his body since birth. The diagnosis of AKC was determined based on a constellation of clinical findings, histopathologic examination with immunohistochemistry, and ultrasound technique. This case provides a photo representation of a rarely reported skin condition in a patient with skin of color and highlights the importance of using multiple diagnostic tools to distinguish AKC from other differential diagnoses.