Reversed Potts Shunt and Venopulmonary Extracorporeal Membrane Oxygenation Support in Sustained Pulmonary

Xiafeng Yu1, Yanjun Sun1, Lijun Fu2

  • 1Department of Cardiothoracic Surgery, Shanghai Children's Medical Center, Shanghai Jiao Tong University School of Medicine, Shanghai, China.

JACC. Case Reports
|September 26, 2025
PubMed

Insights

Infantile idiopathic pulmonary arterial hypertension is a critical condition. Reversed Potts shunt (RPS) and venopulmonary extracorporeal membrane oxygenation (V-P ECMO) offer successful treatment for pulmonary hypertension crises.

Area of Science:

  • Pediatric Cardiology
  • Cardiovascular Surgery
  • Critical Care Medicine

Background:

  • Infantile idiopathic pulmonary arterial hypertension (IPAH) is a rare, life-threatening condition.
  • Recurrent pulmonary hypertensive crises in infants with IPAH carry a high mortality rate.
  • Medical therapy is often insufficient for managing severe pulmonary hypertensive crises.
Abstract

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