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Arrhythmogenic Right Ventricular Cardiomyopathy and Cor Triatriatum Dexter: An Unreported Association

Erica Franco1, Chiara Rovera1, Claudio Moretti1

  • 1Cardiology Division Civic Hospital of Chivasso Turin Italy.

Clinical Case Reports
|October 7, 2025
PubMed

Insights

A rare case of arrhythmogenic right ventricular cardiomyopathy with heart failure also had cor triatriatum dexter. This unusual combination of cardiac conditions was discovered incidentally via echocardiography.

Area of Science:

  • Cardiology
  • Cardiac Imaging
  • Congenital Heart Disease

Background:

  • Arrhythmogenic right ventricular cardiomyopathy (ARVC) is an inherited heart muscle disease.
  • Cor triatriatum dexter is a rare congenital anomaly where the right atrium is divided by a membrane.

Purpose of the Study:

  • To report a unique case of concomitant ARVC and cor triatriatum dexter.
  • To describe the diagnostic approach and management of this rare association.

Main Methods:

  • Echocardiography was used for diagnosis.
  • Clinical presentation and management strategies were reviewed.

Main Results:

  • A 74-year-old patient with ARVC and heart failure was found to have cor triatriatum dexter.
  • This association has not been previously documented in medical literature.

Conclusions:

  • This case highlights the importance of thorough echocardiographic evaluation.
  • Further research may be needed to understand the potential relationship between these conditions.

Keywords:
arrhythmogenic right ventricular cardiomyopathycardiac magnetic resonance imagingcongenital heart diseasecor triatriatum dexterechocardiography

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