Bentall-De Bono Procedure as a Treatment for Stanford Type A Chronic Aortic Dissection

Marfan syndrome is a connective tissue disorder with multisystemic involvement, in which cardiovascular complications, particularly aortic dissection, are the leading cause of mortality. We report a case of a 35-year-old woman with known Marfan syndrome who complained of chest pain in the last 4 months and was found to have a chronic Stanford type A aortic dissection and severe aortic insufficiency. Surgical repair with a Bentall-De Bono procedure was successfully performed. This case highlights the importance of early recognition of chronic dissection in Marfan patients and the effectiveness of surgical management using the current gold standard approach.