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Paraneoplastic pityriasis rubra pilaris: a systematic review
James Gaston1, Andrew Maxwell2, Francis Yi Xing Lai3,4
1Department of Dermatology, The Royal Children's Hospital Melbourne, Melbourne, VIC, Australia.
Clinical and Experimental Dermatology
|October 24, 2025
Summary
Paraneoplastic pityriasis rubra pilaris (PRP), a rare skin condition, is often linked to cancer. Early cancer screening is vital for atypical or treatment-resistant PRP cases, as treating the cancer can resolve the skin condition.
Area of Science:
- Dermatology
- Oncology
- Internal Medicine
Background:
- Paraneoplastic pityriasis rubra pilaris (PRP) is a rare, chronic inflammatory skin disease.
- Its association with underlying malignancy necessitates prompt cancer diagnosis and management.
Conclusions:
- Paraneoplastic PRP is linked to various solid and hematological malignancies.
- Cancer screening is recommended for atypical or refractory PRP.
- Further research is needed to identify predictive features and optimize diagnostic strategies.

