Splenectomy does not improve survival in chronic active Epstein-Barr virus disease patients

Junzhe Wang1, Xiaodan He1, Deli Song1

  • 1Department of Hematology, Beijing Friendship Hospital, Capital Medical University, 95 YongAn Road, Xicheng District, Beijing, 100050, China.

Annals of Hematology
|November 10, 2025
PubMed

Insights

Splenectomy does not reduce Epstein-Barr virus (EBV) DNA levels or improve survival in Chronic Active Epstein-Barr Virus Disease (CAEBVD). This study suggests splenectomy has a limited role in managing CAEBVD patients.

Area of Science:

  • Immunology
  • Virology
  • Surgical Oncology

Background:

  • Chronic Active Epstein-Barr Virus Disease (CAEBVD) is a severe condition requiring effective treatment strategies.
  • Splenectomy is a potential intervention, but its clinical value in CAEBVD remains unclear.
  • Understanding the impact of splenectomy on viral load and patient outcomes is crucial for treatment decisions.

Purpose of the Study:

  • To evaluate the clinical efficacy of splenectomy in managing Chronic Active Epstein-Barr Virus Disease (CAEBVD).
  • To assess the impact of splenectomy on Epstein-Barr virus (EBV) DNA levels and patient survival.
  • To determine if splenectomy influences outcomes in CAEBVD patients, particularly those with Hemophagocytic Lymphohistiocytosis (HLH) or who undergo Allogeneic Hematopoietic Stem Cell Transplantation (Allo-HSCT).

Main Methods:

  • Retrospective review of clinical data from 48 CAEBVD patients (October 2014 - October 2024).
  • A cohort of 16 patients who underwent splenectomy was propensity score matched (1:2 ratio) with 32 non-splenectomy controls.
  • Analysis included EBV-DNA levels, overall survival (OS), recurrence-related death, and engraftment times post-Allo-HSCT.

Main Results:

  • Splenectomy did not significantly reduce peripheral blood EBV-DNA copies.
  • There was no statistically significant difference in median overall survival between the splenectomy (86 months) and non-splenectomy (23 months) groups (P=0.189).
  • No significant benefits were observed in symptom relief, survival time after recurrence-related death, or engraftment times in patients undergoing Allo-HSCT.

Conclusions:

  • Splenectomy shows no significant benefit in reducing EBV viral load or improving symptom relief in CAEBVD.
  • The procedure does not appear to prolong patient survival, indicating a limited role in CAEBVD management.
  • Further research may be needed to explore alternative or adjunctive therapies for CAEBVD.