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Related Concept Videos

Cardiomyopathy VII: Pre and Post Operative Nursing Management01:28

Cardiomyopathy VII: Pre and Post Operative Nursing Management

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Patients with hypertrophic cardiomyopathy (HCM) and left ventricular outflow tract (LVOT) obstruction who remain symptomatic despite optimal medical therapy may undergo a septal myectomy (Morrow procedure). This procedure involves excising a portion of the hypertrophied septum below the aortic valve using a heart-lung machine to improve blood flow through the LVOT. Effective preoperative and postoperative nursing management ensures successful patient outcomes, minimizes complications, and...
264
Mitral Stenosis III: Medical Management01:26

Mitral Stenosis III: Medical Management

224
Mitral stenosis, a condition marked by the narrowing of the mitral valve, necessitates an integrated approach for effective management. This approach includes preventative measures, medical therapy, and surgical interventions to reduce symptoms and prevent complications.PreventionPrevention of mitral stenosis primarily focuses on reducing the incidence of bacterial infections, particularly streptococcal infections, which can lead to rheumatic fever and subsequent valvular damage. Timely...
224
Mitral Regurgitation III: Medical Management01:25

Mitral Regurgitation III: Medical Management

258
Mitral regurgitation (MR) is characterized by retrograde blood circulation from the left ventricle into the left atrium due to inadequate mitral valve closure. The severity of the condition, symptoms, and underlying cause determine treatment strategies.Monitoring and Pharmacological TreatmentPatients with mild to moderate MR typically do not need immediate intervention but regular monitoring to assess progression and guide treatment. Patients with mild MR should have an echocardiogram every 3-5...
258
Cardiomyopathy V: Interprofessional Care01:29

Cardiomyopathy V: Interprofessional Care

316
Managing cardiomyopathy involves addressing underlying or precipitating causes, treating heart failure with medications, and implementing dietary changes and a balanced exercise and rest regimen.Lifestyle ModificationsCardiomyopathy patients should adopt a low-sodium diet to reduce fluid retention and manage heart failure. A personalized exercise and rest plan helps maintain physical fitness without overstraining the heart. Avoiding alcohol and tobacco is essential to prevent further damage to...
316
Cardiomyopathy III: Hypertrophic Cardiomyopathy01:29

Cardiomyopathy III: Hypertrophic Cardiomyopathy

378
Hypertrophic cardiomyopathy, or HCM, is an autosomal dominant genetic disorder characterized by asymmetric left ventricular hypertrophy without ventricular dilation. It is more common in men and is typically diagnosed in young, athletic adults.EtiologyHCM is primarily genetic and is caused by mutations in genes encoding sarcomeric proteins. Researchers have identified over 1400 mutations across at least 11 different genes. Among these, the most frequently occurring mutations are found in the...
378
Mitral Stenosis I: Introduction01:22

Mitral Stenosis I: Introduction

420
Mitral Valve Stenosis (MVS) is a heart condition where the mitral valve narrows, impeding blood circulation from the left atrium to the left ventricle. The etiology and pathophysiology of this condition are multifaceted, leading to a cascade of cardiovascular complications.Causes of Mitral Valve StenosisRheumatic Heart Disease: It is the main cause of mitral valve stenosis, particularly in developing nations. This condition arises from rheumatic fever, an inflammatory illness resulting from...
420

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Biventricular Surgical Approach in Noonan Syndrome With Hypertrophic Obstructive Cardiomyopathy.

Ryo Fujimoto1, Shingo Hirao1, Tatsuhiko Komiya1

  • 1Department of Cardiovascular Surgery, Kurashiki Central Hospital, Kurashiki, Japan.

JACC. Case Reports
|November 25, 2025
PubMed
Summary

Noonan syndrome patients with hypertrophic obstructive cardiomyopathy may require complex surgical interventions. Dual ventriculotomy approaches offer improved access for effective myectomy in challenging cases.

Area of Science:

  • Cardiology
  • Cardiovascular Surgery
  • Genetics

Background:

  • Noonan syndrome frequently presents with cardiac anomalies, including pulmonary valve stenosis, hypertrophic cardiomyopathy, and atrial septal defects.
Keywords:
Noonan syndromehypertrophic obstructive cardiomyopathyleft ventriculotomyright ventriculotomyseptal myectomy

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  • Hypertrophic cardiomyopathy (HCM) is a significant concern in Noonan syndrome, potentially leading to obstructive complications.