Ischemic Heart Disease With Right Ventricular Involvement Mimicking Arrhythmogenic Right Ventricular Cardiomyopathy

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a heritable heart disease that predisposes to sudden cardiac death. Diagnosis is challenging given the lack of specificity of diagnostic criteria and disease mimics. Cardiac magnetic resonance contributes to the diagnosis of ARVC through its advanced assessment of the right ventricle. We describe a 76-year-old woman who met 3 major and 1 minor diagnostic criteria of ARVC, including a major criterion on cardiac magnetic resonance. These criteria only emerged after severe right ventricular infarct 8 years prior. This case highlights the importance of considering mimics when suspecting ARVC even if diagnostic criteria suggest a definite diagnosis.