Erdheim-Chester Disease: A Rare Presentation With Atrial Flutter and Severe Sinus Node Dysfunction.

Yazeed G Alqurashi1, Atheer A Al-Qurashi2, Rana M Ajabnoor3

  • 1Cardiology Department, King Abdulaziz Medical City, Ministry of National Guard Health Affairs, Jeddah, Saudi Arabia; King Abdullah International Medical Research Center, Jeddah, Saudi Arabia.

JACC. Case Reports
|April 11, 2026
PubMed
Summary

Erdheim-Chester disease (ECD) can present with arrhythmias, highlighting the need for thorough cardiac evaluation. Early management with pacing and targeted therapy improves outcomes for patients with cardiovascular involvement.

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