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Awareness and knowledge gaps about pediatric rare disease among anesthesia practitioners in China: a survey-based
Yan Ming Kang1,2, Zhen Xia3, Xiang Li1,2
1Department of Anesthesiology, West China Second University Hospital, Sichuan University, No. 20, Sect. 3 People South Road, Chengdu, 610041, China.
Insights
Anesthesia providers in China show significant gaps in knowledge and confidence for managing pediatric rare diseases. Enhanced training and support systems are urgently needed for this patient population.
Area of Science:
- Anesthesiology
- Pediatric Rare Diseases
- Healthcare Education
Background:
- Pediatric patients with rare diseases pose unique anesthetic challenges.
- Anesthesia practitioners require specialized knowledge for safe perioperative care.
- This study assesses competency and educational needs in China.
Purpose of the Study:
- To evaluate the clinical competency of anesthesia practitioners in China.
- To identify specific educational needs for managing pediatric rare diseases.
- To inform the development of better support systems.
Main Methods:
- A cross-sectional survey was conducted among 2127 anesthesia practitioners in China.
- Data collected via anonymous questionnaire from May 2024 to March 2025.
- Descriptive statistics and chi-square tests were used for analysis.
Main Results:
- Most practitioners (43.2%) had experience with rare pediatric diseases, but self-assessed competency was low (9.0% comprehensive knowledge, 15.0% confident).
- Significant knowledge deficits were found in specific areas like contraindications (14.9%), difficult airways (6.6%), and drug risks (3.9%).
- Clinical exposure correlated with better understanding; practitioners requested comprehensive diagnostic info (58.6%) and contraindications (57.0%), plus real-time updates (50.1%).
Conclusions:
- Substantial knowledge gaps and low confidence exist among Chinese anesthesia providers for pediatric rare disease management.
- There is an urgent need for improved training programs.
- Development of robust, updated support systems is crucial for this vulnerable patient group.
Background:
Anesthetic management of pediatric patients with rare diseases presents substantial perioperative challenges and risks. This study evaluated the clinical competency and specific educational needs of anesthesia practitioners in China regarding the perioperative management of this vulnerable patient population.
Method:
A cross-sectional survey was conducted from May 2024 and March 2025, involving 2127 anesthesia practitioners across China. Data were collected via a validated anonymous questionnaire and analyzed through descriptive statistics and chi-square tests.
Result:
Among the 2,127 participants, 93.5% were anesthesiologists and 6.5% were nurse anesthetists. Of these, 43.2% (919/2127) reported previous experience in administering anesthesia to children with rare diseases. Despite this exposure, self-assessed competency levels were notably insufficient. Only 9.0% (191/2127) of respondents reported comprehensive knowledge of pediatric rare diseases, and 15.0% (318/2127) expressed adequate confidence in perioperative management protocols. Objective assessment of specific knowledge domains revealed considerable deficiencies: 14.9% (317/2127) of respondents correctly identified contraindications in muscular dystrophy, 6.6% (141/2127) demonstrated adequate understanding of difficult airway indicators, and merely 3.9% (82/2127) accurately recognized depolarizing agent risks. Comparative analysis between self-rated high-familiarity and low-familiarity groups revealed that direct clinical exposure was significantly associated with practitioners' understanding of pediatric rare diseases. Regarding the development of future anesthesia support systems for pediatric rare diseases, practitioners identified two primary requirements: comprehensive diagnostic information (58.6%, 1246/2127) and detailed anesthesia contraindications (57.0%, 1212/2127). Additionally, 50.1% (1065/2127) of respondents emphasized the importance of real-time knowledge base updates to ensure access to current clinical guidelines and safety protocols.
Conclusion:
This study highlights substantial knowledge gaps and insufficient confidence among anesthesia practitioners in the perioperative management of children with rare diseases, underscoring an urgent need for enhanced training and robust support systems in this specialized area.
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