Bilateral Coronary Ostial Atresia: A Malignant Anatomic Variant
Jose Morales Hernandez1, Utkarsh Kohli2, Daniel Duarte2
1Department of Pediatrics, Nicklaus Children's Hospital, Miami, Florida, USA.
JACC. Case Reports
|May 19, 2026
Summary
Bilateral coronary ostial atresia (BCOA) is a rare congenital heart defect with a poor prognosis. This case highlights a unique BCOA variant with a malignant clinical course, emphasizing the need for early detection and intervention.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Disease
- Cardiac Surgery
Background:
- Bilateral coronary ostial atresia (BCOA) is an exceedingly rare congenital cardiac anomaly.
- Outcomes and clinical characteristics of BCOA are poorly understood due to its rarity.
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