Spontaneously Resolving Pancreatic IgG4-Related Disease Representing With Systemic Involvement and Membranous

Iwan G A Raza1, Stuart W Smith1, Dimitrios Chanouzas1,2

  • 1Department of Renal Medicine, Queen Elizabeth Hospital, Birmingham, United Kingdom.

Kidney Medicine
|May 28, 2026
PubMed
Summary

Immunoglobulin G4-related disease (IgG4-RD) can cause secondary membranous nephropathy (MN) without kidney inflammation. This case highlights IgG4-RD presenting as nephrotic syndrome, successfully treated with steroids and rituximab.

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