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An Unusual Etiology of Bayés' Syndrome: Fabry Disease

Nicholas E Kunce1, Andre Silva1, Mark Haigney2

  • 1Department of Medicine, Division of Cardiology, Brooke Army Medical Center, Fort Sam Houston, Texas, USA.

Annals of Noninvasive Electrocardiology : the Official Journal of the International Society for Holter and Noninvasive Electrocardiology, Inc
|July 1, 2026
PubMed

Insights

This case report details a 72-year-old female with Fabry disease experiencing Bayés

Area of Science:

  • Cardiology
  • Genetics
  • Rare Diseases

Background:

  • Fabry disease is an X-linked lysosomal storage disorder.
  • Globotriaosylceramide accumulation in Fabry disease can affect cardiac function.
  • Cardiac conduction disease is a known complication of Fabry disease.

Keywords:
Bayés' syndromeFabry diseaseatrial fibrillationinfiltrative cardiomyopathyinteratrial blocklysosomal storage disorder

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