Congenital retroperitoneal hemangioendothelioma with Kasabach-Merritt syndrome

This is the first documented congenital retroperitoneal hemangioendothelioma. The patient presented at birth with a retroperitoneal mass and thrombocytopenia. Postmortem examination revealed the tumor to be a hemangioendothelioma, arising from the posterior abdominal wall. The association of an angiomatous tumor will thrombocytopenia represents the Kasabach-Merritt syndrome.