[Multiple enchondromas of both hands with ulna hypoplasia and radius dysplasia on the left]

A 33 year old patient with multiple enchondromas of both hands, ulna hypoplasia and radial dysplasia is described. In addition, a deformity of ulna and radius was present on the left side. The first signs of the disease appeared in 1949. The diagnosis, made by biopsy and X-ray was the indication for surgery. The result was very satisfactory. The differences of this undescribed syndrome from Morbus Ollier disease are discussed.