Combined double chambered right ventricle and discrete subaortic stenosis

Nine cases of combined double-chambered right ventricle (DCRV) and discrete subaortic stenosis (DSAS) are presented. A review of 1077 consecutively catheterized patients indicates an association of these two uncommon anomalies nine times greater than expected. One or both obstructive lesions may be hemodynamically significant and require surgery. Whenever DCRV or DSAS is suspected or identified, the cardiac catheterization should include studies of both the right and left ventricles.