[Patient with factor V deficiency (parahemophilia) diagnosed and treated as hemophilia A]

The authors observed the patient T.P.D., aged 36, admitted to the clinic of RIHBT with melena and hematemesis. Since early childhood the patient has been treated on the occasions of hemorrhagic incidences for hemophilia A. The hemostatic investigations however, revealed normal level of factor VIII and the level of factor V--1%, providing grounds to revise the initial diagnosis and to admit that the rarely found parahemophilia is concerned. The treatment with freshly-frozen plasma, fresh blood, velin and iron preparations led to coping with hemorrhagic syndrome and posthemorrhagic anemia. The diagnostic possibilities are interpreted for establishing the deficiency of the factors of coagulation and of the specific substitution therapy.