Aortic insufficiency in Reiter's syndrome of juvenile onset

Reiter's syndrome is an uncommon cause of childhood arthritis and aortic incompetence is extremely rare in these patients. A 7-year-old boy with Reiter's syndrome and hemodynamically significant aortic insufficiency is reported. He was HLD-B27 positive and valvular incompetence was detected 32 months after the onset while active synovitis was still present.