Amyloidosis complicating cystic fibrosis

A 33-year-old white man with cystic fibrosis and severe chronic pulmonary disease developed nephrotic syndrome and was found to have secondary systemic amyloidosis. Only four such cases have been reported in the English literature. Previously reported cases are reviewed and compared. It is suggested that with increasing longevity in cystic fibrosis, more amyloidosis may be seen.